Progressive facial hemiatrophy with localized scleroderma.
نویسندگان
چکیده
A 46-year-old woman who presented with progressive facial hemiatrophy (PFH) following localized scleroderma is described. The patient had a markedly deformed and depressed plaque surrounded by erythema on the right cheek. She also showed linear scleroderma with hair loss on the occipital area and morphea lesions on the neck and shoulder. Histological findings of the facial and other atrophic lesions were consistent with localized scleroderma. Therefore, the PFH and localized scleroderma may have had the same pathological background in this case.
منابع مشابه
Progressive Facial Hemiatrophy. (parry--romberg Syndrome). (a Case Report).
Progressive facial hemiatrophy or Parry-Romberg Syndrome is a rare disease characterized by atrophy in subcutaneous tissues on skin on one half of the face and some accompanied systematic findings. Generally, it develops before the age of 20. It is quite difficult to discriminate it from linear scleroderma localized in fronto-parietal area as they have similar clinical characteristics. In this ...
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ورودعنوان ژورنال:
- The Tokai journal of experimental and clinical medicine
دوره 17 2 شماره
صفحات -
تاریخ انتشار 1992